Annals of Indian Academy of Neurology
REVIEW ARTICLE
Year
: 2007  |  Volume : 10  |  Issue : 5  |  Page : 55--58

Sturge-Weber syndrome


Sarah Aylett 
 Great Ormond Street Hospital for Children, London and National Centre for Young People with Epilepsy, Lingfield, United Kingdom

Correspondence Address:
Sarah Aylett
Great Ormond Street Hospital for Children, London and National Centre for Young People with Epilepsy, Lingfield
United Kingdom

Sturge-Weber syndrome (SWS) is characterized by a facial capillary hemangioma (port wine stain) involving the periorbital area, forehead or scalp, a venous angioma of the leptomeninges and a choroidal angioma. Following normal early development, children with SWS often experience neurological and developmental deterioration in association with the onset of seizures and consequently suffer a high rate of disability. The classical imaging finding in these children is the evidence of calcification in the occipital area. The striking features of the EEG in SWS are the attenuation and the excess of slow activities. Recent advances in the diagnosis and treatment, particularly the surgical options are discussed.


How to cite this article:
Aylett S. Sturge-Weber syndrome.Ann Indian Acad Neurol 2007;10:55-58


How to cite this URL:
Aylett S. Sturge-Weber syndrome. Ann Indian Acad Neurol [serial online] 2007 [cited 2020 Sep 22 ];10:55-58
Available from: http://www.annalsofian.org/article.asp?issn=0972-2327;year=2007;volume=10;issue=5;spage=55;epage=58;aulast=Aylett;type=0