Annals of Indian Academy of Neurology
CASE REPORT
Year
: 2009  |  Volume : 12  |  Issue : 2  |  Page : 124--126

Primary Sjögren俟Q製 syndrome manifesting as multiple cranial neuropathies: MRI findings


VV Ashraf1, Ramesh Bhasi2, R Praveen Kumar1, AS Girija1 
1 Department of Neurology, Malabar Institute of Medical Sciences, Calicut - 673 016, Kerala, India
2 Department of Rheumatology, Malabar Institute of Medical Sciences, Calicut - 673 016, Kerala, India

Correspondence Address:
V V Ashraf
Department of Neurology, Malabar Institute of Medical Sciences, Calicut - 673 016, Kerala
India

We report a case of primary Sjögren俟Q製 syndrome presenting with multiple cranial nerve palsies and radiological evidence of cranial pachymeningitis and hypophysitis. A 47-year-old woman developed right sensory neural hearing loss followed, 2 months later, by right facial palsy. Cranial magnetic resonance imaging showed features of pachymeningitis and pituitary gland infiltration. The diagnosis of primary Sjögren俟Q製 syndrome was confirmed by demonstrating positive SS-A and SS-B antibodies and histological evidence of lymphocytic infiltration of the sublabial salivary gland. During the 2-year follow-up, the patient had transient VI th , IX th , X th , and XII th cranial nerve palsies. Sjögren俟Q製 syndrome should be considered in the differential diagnosis of patients presenting with multiple recurrent cranial nerve palsies, even if prominent sicca symptoms are absent.


How to cite this article:
Ashraf V V, Bhasi R, Kumar R P, Girija A S. Primary Sjögren's syndrome manifesting as multiple cranial neuropathies: MRI findings.Ann Indian Acad Neurol 2009;12:124-126


How to cite this URL:
Ashraf V V, Bhasi R, Kumar R P, Girija A S. Primary Sjögren's syndrome manifesting as multiple cranial neuropathies: MRI findings. Ann Indian Acad Neurol [serial online] 2009 [cited 2020 Aug 7 ];12:124-126
Available from: http://www.annalsofian.org/article.asp?issn=0972-2327;year=2009;volume=12;issue=2;spage=124;epage=126;aulast=Ashraf;type=0